Rheumatology · Pathway 22
Mixed Connective Tissue Disease
Key points
- Mixed connective tissue disease (MCTD, Sharp's syndrome) is a rare, heterogeneous, multi-system autoimmune disorder. It is a distinct clinical entity, but features of systemic lupus erythematosus (SLE),
- Male:female ratio 1:3
- Average age of presentation 30-40, may present in children
- Rare - incidence in adult population is estimated to be 2.1/million/year in one Norwegian study Presentation:
- Raynaud's phenomenon often precedes other symptoms and occurs in 90% of cases