Pulmonology · Pathway 7
Kartagener's Syndrome
Key points
- Kartagener's syndrome Kartagener's syndrome (also known as primary ciliary dyskinesia) was first described in 1933 and most frequently occurs in examinations due to its association with dextrocardia (e.g. 'quiet heart sounds',
- dynein arm defect results in immotile cilia Features
- dextrocardia or complete situs inversus
- bronchiectasis
- recurrent sinusitis