Pulmonology · Pathway 53
Eosinophilic Granulomatosis with Polyangiitis
Key points
- Eosinophilic granulomatosis with polyangiitis (Churg-Strauss syndrome) Eosinophilic granulomatosis with polyangiitis (EGPA) is now the preferred term for Churg-Strauss syndrome.
- blood eosinophilia (e.g. > 10%)
- paranasal sinusitis
- mononeuritis multiplex
- pANCA positive in 60% Granulomatosis with polyangiitis (Wegener's granulomatosis) Churg-Strauss syndrome Vasculitis Renal failure Asthma Sinusitis Epistaxis I haemoptysis pANCA Dyspnoea EosmopNlia cANCA Comparison of…