Pulmonology · Pathway 32
Idiopathic Pulmonary Fibrosis
Key points
- Idiopathic pulmonary fibrosis Idiopathic pulmonary fibrosis (IFF, previously termed cryptogenic fibrosing alveolitis) is a chronic lung condition characterised by progressive fibrosis of the interstitium of the lungs.
- progressive exertional dyspnoea
- bibasal fine end-inspiratory crepitations on auscultation
- clubbing Diagnosis
- spirometry: classically a restrictive picture (FEV1 normal/decreased, FVC decreased, FEV1/FVC increased)