Dubin-Johnson Syndrome

Key points

• Dubin-Johnson syndrome is a benign autosomal recessive disorder resulting in hyperbilirubinaemia (conjugated, therefore present in urine).
• Dubin-Johnson syndrome is a benign autosomal recessive
• disorder resulting in hyperbilirubinaemia (conjugated,
• therefore present in urine). It is due to a defect in the
• canillicular multispecific organic anion transporter (cMOAT)